Ortner's syndrome

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Image:Gray505.png
Image of aortic anatomy showing proximity of vagus nerve and its recurrent branch to the aorta

Ortner's syndrome is a rare cardiovocal syndrome and refers to recurrent laryngeal nerve palsy from cardiovascular disease [1]. It was first described by N. Ortner, an Austrian physician, in 1897.

The most common historical cause is a dilated left atrium due to mitral stenosis, but other causes, including pulmonary hypertension[2], thoracic aortic aneurysms and aberrant subclavian artery syndrome have been reported [3].

Dysphagia caused by a similar mechanism is referred to as dysphagia aortica, or, in the case of subclavian artery aberrancy, as dysphagia lusoria.

A second Ortner's syndrome, Ortner's syndrome II, refers to abdominal angina.

References

  1. Bickle IC et al., Ortner's Syndrome. The Ulster Medical Journal. 71(1) 55-56 [1]
  2. Hermans C et al. Ortner syndrome and haemophilia. Haemophilia. 2005 Sep;11(5):548-51. [2]
  3. Escribano JF et al. Ortner's syndrome and endoluminal treatment of a thoracic aortic aneurysm: a case report. Vasc Endovascular Surg. 2006 Jan-Feb;40(1):75-8. [3]

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